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Product Name
Galactosidase alpha Rabbit mAb
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Gene ID
2717
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SwissProt ID
P06280
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Gene Name
GLA
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Alternative Names
Alpha gal A; GALA; Galactosidase; alpha; GLA; Melibiase
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Background
Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.
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Research Field
Cardiovascular
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Product Categories
Primary antibody
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Host
Rabbit
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Reactivity
Human
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Application
WB,IHC-P,IP
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Dilution Ratio
WB: 1/500-1/1000 IHC: 1/50-1/100 IP: 1/20
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Molecular Weight
Calculated MW: 49 kDa; Observed MW: 49 kDa
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Clonality
Monoclonal Antibody
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Clonality No.
R01-9J4
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Isotype
IgG
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Immunogen
A synthetic peptide of human Galactosidase alpha
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Purification
Affinity Purified
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Conjugation
Unconjugated
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Modification
Unmodified
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Form
Liquid
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Buffer System
50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% Sodium azide and 0.05% BSA
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Storage
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles.