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货号： 240118

别名： PBD2A; PBD2B; PTS1-BP; PTS1R; PXR1; RCDP5

应用： WB

反应种属： Human,Monkey,Mouse,Rat

目录价格：

RMB(含税报价)

数量： - + （库存件）

查看代理商预计货期：3-4个工作日说明书PDF

产品详情

Product Name

[KO] PEX5 Mouse mAb
Gene ID

5830
SwissProt ID

P50542
Gene Name

PEX5
Alternative Names

PBD2A; PBD2B; PTS1-BP; PTS1R; PXR1; RCDP5
Background

The product of this gene binds to the C-terminal PTS1-type tripeptide peroxisomal targeting signal (SKL-type) and plays an essential role in peroxisomal protein import. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of neonatal adrenoleukodystrophy (NALD), a cause of Zellweger syndrome (ZWS) as well as may be a cause of infantile Refsum disease (IRD). Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq]
Research Field

Signal Transduction
Product Categories

KO/KD validated
Host

Mouse
Reactivity

Human,Monkey,Mouse,Rat
Application

WB
Dilution Ratio

WB: 1/500-1/1000
Molecular Weight

Calculated MW: 71 kDa; Observed MW: 80 kDa
Clonality

Monoclonal Antibody
Clonality No.

6000000000
Isotype

IgG1
Immunogen

Full length human recombinant protein of human PEX5 produced in 293T cell.
Purification

Affinity Purified
Conjugation

Unconjugated
Modification

Unmodified
Form

Liquid
Buffer System

Liquid in PBS containing 50% glycerol, 1% BSA and 0.02% sodium azide, pH 7.3.
Storage

Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles.

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验证详情

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应用缩写

WB:蛋白质印迹法IHC-P:石蜡切片样本的免疫组织化学法IHC-F:冰冻切片样本的免疫组织化学法ICC/IF:免疫细胞荧光 IP:免疫沉淀法FC:流式细胞术ChIP:染色质免疫沉淀法ELISA:酶联免疫吸附测定正能生物产品售后保障范围仅限官网产品详情页中“应用”一栏写明的实验应用，请参照上方的缩写含义，仔细对照后选择合适的产品。

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